GSD Type VI and IX (Hers and Phosphorylase Kinase) Severity

Assesses glycogen storage disease types VI (liver phosphorylase) and IX (phosphorylase kinase) severity using hypoglycemia frequency, ketosis, growth, and liver function for dietary management guidance.

Weight
Height
Clinical Guidance

BMI is a screening measure of body size, not a direct measure of body fat. The standard WHO categories are underweight (<18.5), normal (18.5–24.9), overweight (25–29.9), and obese (≥30).

BMI can overestimate body fat in athletes with high muscle mass and underestimate it in older adults with low muscle mass. Interpret it alongside waist circumference and clinical context rather than as a standalone diagnosis.

⚕ Clinical Disclaimer: These calculators are for educational and reference purposes only. Always verify results with qualified clinical judgment and current clinical guidelines. Do not use as a sole basis for medical decisions.
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How It Works

Assesses glycogen storage disease types VI (liver phosphorylase) and IX (phosphorylase kinase) severity using hypoglycemia frequency, ketosis, growth, and liver function for dietary management guidance

Each component has a specific meaning:

  • Hypoglycemia frequency — The hypoglycemia frequency recorded for the scenario being assessed.
  • Ketosis — The ketosis recorded for the scenario being assessed.
  • Growth — The growth recorded for the scenario being assessed.
  • Liver function — The liver function recorded for the scenario being assessed.

Note: Interpret the gsd vi/ix severity result against the thresholds and context described above.

How to Use

Enter the hypoglycemia frequency, ketosis, growth, liver function for the scenario you are assessing. Assesses glycogen storage disease types VI (liver phosphorylase) and IX (phosphorylase kinase) severity using hypoglycemia frequency, ketosis, growth, and liver function for dietary management guidance. Use the gsd vi/ix severity result to inform your calculation.

Frequently Asked Questions