Neuronal Ceroid Lipofuscinosis (Batten Disease) Clinical Staging

Stages neuronal ceroid lipofuscinosis (CLN1-14) using HAMBURGS unified Batten disease rating scale, PPT1/TPP1 enzyme activity confirmation, and cerliponase alfa (CLN2) dosing and infusion monitoring.

Weight
Height
Clinical Guidance

BMI is a screening measure of body size, not a direct measure of body fat. The standard WHO categories are underweight (<18.5), normal (18.5–24.9), overweight (25–29.9), and obese (≥30).

BMI can overestimate body fat in athletes with high muscle mass and underestimate it in older adults with low muscle mass. Interpret it alongside waist circumference and clinical context rather than as a standalone diagnosis.

⚕ Clinical Disclaimer: These calculators are for educational and reference purposes only. Always verify results with qualified clinical judgment and current clinical guidelines. Do not use as a sole basis for medical decisions.
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How It Works

Stages neuronal ceroid lipofuscinosis (CLN1-14) using HAMBURGS unified Batten disease rating scale, PPT1/TPP1 enzyme activity confirmation, and cerliponase alfa (CLN2) dosing and infusion monitoring

Each component has a specific meaning:

  • HAMBURGS unified Batten disease rating scale — The hamburgs unified batten disease rating scale recorded for the scenario being assessed.
  • PPT1/TPP1 enzyme activity confirmation — The ppt1/tpp1 enzyme activity confirmation recorded for the scenario being assessed.
  • Cerliponase alfa dosing — The cerliponase alfa dosing recorded for the scenario being assessed.
  • Infusion monitoring — The infusion monitoring recorded for the scenario being assessed.

Note: Interpret the ncl staging result against the thresholds and context described above.

How to Use

Enter the HAMBURGS unified Batten disease rating scale, PPT1/TPP1 enzyme activity confirmation, cerliponase alfa dosing, infusion monitoring for the scenario you are assessing. Stages neuronal ceroid lipofuscinosis (CLN1-14) using HAMBURGS unified Batten disease rating scale, PPT1/TPP1 enzyme activity confirmation, and cerliponase alfa (CLN2) dosing and infusion monitoring. Use the ncl staging result to inform your calculation.

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