Monitors propionic acidemia metabolic control using plasma propionylcarnitine, ammonia, bicarbonate, and ketones with recommendations for biotin and carnitine supplementation and cardiac surveillance.
Monitors propionic acidemia metabolic control using plasma propionylcarnitine, ammonia, bicarbonate, and ketones with recommendations for biotin and carnitine supplementation and cardiac surveillance
Each component has a specific meaning:
Note: Interpret the pa monitor result against the thresholds and context described above.
Enter the plasma propionylcarnitine, ammonia, bicarbonate, ketones for the scenario you are assessing. Monitors propionic acidemia metabolic control using plasma propionylcarnitine, ammonia, bicarbonate, and ketones with recommendations for biotin and carnitine supplementation and cardiac surveillance. Use the pa monitor result to inform your calculation.